SynonymsBot
Synonyms for tgfbi or Related words with tgfbi
tagln
plaur
cebpd
nfib
thbd
cklf
tyrobp
pdgfb
postn
hemgn
pdgfc
rragd
nfic
vcan
hnrnpc
vegfb
ptprk
prkaca
pdgfrl
pdgfa
srgn
oplah
nucks
hbegf
ptgis
narfl
procr
nudc
tnxb
tpbg
ywhab
dgka
nfkbie
nfkbib
ptprd
emcn
ptprc
heph
myof
frzb
mdfic
snrpa
ptprm
dgkb
lpxn
agrn
syncrip
enah
hhip
tdrkh
Examples of "tgfbi"
The gene
TGFBI
encodes the protein keratoepithelin.
Transforming growth factor, beta-induced, 68kDa, also known as
TGFBI
(initially called BIGH3, BIG-H3), is a protein which in humans is encoded by the "
TGFBI
" gene, locus 5q31.
Some cases of it are linked to chromosome 10q24, others stem from a mutation in the
TGFBI
gene.
The disease has been associated with mutations in
TGFBI
gene on chromosome 5q which encodes for keratoepithelin. The inheritance is autosomal dominant.
Different corneal dystrophies are caused by mutations in the CHST6, KRT3, KRT12, PIP5K3, SLC4A11, TACSTD2,
TGFBI
, and UBIAD1 genes. Mutations in TGFB1 which encodes "transforming growth factor beta" cause several forms of corneal dystrophies including granular corneal dystrophy, lattice corneal dystrophy, epithelial basement membrane dystrophy, Reis-Bucklers corneal dystrophy, and Thiel–Behnke dystrophy.
In some families autosomal dominant inheritance and point mutations in the
TGFBI
gene encoding keratoepithelin have been identified, but according to the International Committee for Classification of Corneal Diseases (IC3D) the available data still does not merit a confident inclusion of EBMD in the group of corneal dystrophies. In view of this, the more accurate designation of the disease is possibly not dystrophy but "corneal degeneration".
Granular corneal dystrophy is caused by a mutation in the
TGFBI
gene, located on chromosome 5q31. The disorder is inherited in an autosomal dominant manner. This indicates that the defective gene responsible for the disorder is located on an autosome (chromosome 5 is an autosome), and only one copy of the gene is sufficient to cause the disorder, when inherited from a parent who has the disorder.