SynonymsBot
Synonyms for xmea or Related words with xmea
xanthinuria
xanthogranulomatous
xlag
nephronophthisis
ibmpfd
acrocallosal
lhon
fraxa
nonsyndromic
edmd
idomim
arpkd
fraxe
progeria
includedgene
hgps
alagille
hypophosphatasia
iosca
wtmolesbayhydrol
narp
fxtas
jsrd
manbb
fshd
xlh
autosomalrecessive
dyskeratosis
progeroid
adpkd
cerebrotendinous
sclerosteosis
cardiofacial
proteininteracting
nipbl
fukutin
mngie
lincl
frataxin
fsgs
oculopharyngodistal
emerin
autosomaldominant
spartin
sarcoglycan
fcyt
optn
rpgr
mentalretardation
myodystrophy
Examples of "xmea"
X-linked myopathy with excessive autophagy (
XMEA
) is a rare childhood onset disease characterized by slow progressive vacuolation and atrophy of skeletal muscle. There is no known cardiac or intellectual involvement.
X-linked myopathy with excessive autophagy is a rare genetic disease resulting from mutations in the VMA21 gene. The disease has a childhood onset and results in a slowly progressive muscle weakness, typically beginning in the legs, and some patients can eventually require wheelchair assistance with advanced age. The Vma21 protein assists in assembly of the V-ATPase, and
XMEA
associated mutations result in decreased activity of the V-ATPase and increased lysosomal pH.